Congenital malformation of external auditory canal in children
Keywords:
anomaly, atresia, stenosis, external auditory canal, auditory ossiclesAbstract
Congenital anomaly of the external auditory canal is a relatively rare clinical presentation and consists of a number of malformations of the pinna and external auditory canal, the latter ranging from slight narrowing (stenosis) to complete absence of the external auditory canal. Congenital stenosis and atresia of the external auditory canal (EA) are the most common malformations of the external ear. Congenital stenosis and atresia of the ESP are often combined with microtia, anomalies of the middle ear, and facial skeleton, but can also be observed in isolation. The prevalence of congenital atresia of the external auditory canal is 0.83–17.4 per 10,000 births. According to various researchers, this pathology occurs with a frequency of 1 case per 10,000–20,000 newborns. The incidence of congenital auditory atresia, alone or in combination with malformations of the outer, middle and (rarely) inner ear, is estimated at 1:10,000. Atresia of the external auditory canal is in most cases unilateral; the right side is more often affected in males. It can occur as an isolated condition or in association with other congenital anomalies or syndromic disorders such as Goldenhar syndrome, Treacher-Collins syndrome, and trisomy 21.
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